Zusammenfassung der Ressource
Sickle Cell Disease
- genetic disorder
- autosomal recessive
- abnormal hemoglobin
- causes chronic hemolytic
anemia
- Life expectancies mid 40s
- better care increases life expectancy
- Incidence
- 1:400-600 blacks
- 1:1000 Hispanics
- also India, Middle East , and
Mediterranean individuals
- Disease Complications
- infarction of lungs, kidneys,
spleen, and bones
- Painful Leg Ulcers
- dactylitis
- Priapism
- Renal failure
- increased risk of infection
- pneumococcal
- salmonella osteomyelitis
- Diagnosis