Zusammenfassung der Ressource
soft tissue sarcomas
- rhabdomyosarcoma
- commonest form of
soft tissue sarcoma in
childhood
- origin= primitive mesenchymal tissue
- wide variety of primary sites
- varied presentations & prognosis
- clinical features
- head & neck
- commonest sites of disease (40%)
- presentation
- proptosis
- nasal
obstruction
- blood
stained
nasal
discharge
- genitourinary tumours
- organs & sys
- bladder
- female GU tract
- paratesticular strucs
- sx
- dysuria
- urinary obstruction
- scrotal mass
- blood stained
vaginal discharge
- metastatic disease
- assoc w/ poor prognosis
- lung
- liver
- bone
- bone marrow
- present in about 15% of pts at diag
- Ix
- biopsy
- full radiological assessment