Motor Neuron Disease

What is the most common form of Motor Neuron Disease?

Which type of motor neuron disease exhibits both upper and lower motor neuron degeneration?

Which type fo Motor Neuron Disease is also referred to as Lou Gehrig's Disease?

Amyotrophic Lateral Sclerosis typically presents at what age?

The average survival for patients diagnosed with ALS is [blank_start]2-4[blank_end] years, with most eventually dying of [blank_start]respiratory[blank_end] failure

The most common symptoms of onset in ALS are spinal onset and bulbar onset. Match the type of onset to its symptoms: [blank_start]Spinal onset (65%)[blank_end] = Presents with progressive weakness in the arms and the legs [blank_start]Bulbar onset (25%)[blank_end] = Presents with progressive weakness in the muscles of speech, chewing & swallowing.

Which of the following describe Babinski sign

A clonic jaw reflex would suggest which type of ALS onset?

The hands can be a prime indicator of ALS. Split hand syndrome seen in ALS describes the preferential wasting of the [blank_start]thenar[blank_end] muscle group.

Primary Lateral Sclerosis differs from Amyotrophic Lateral Sclerosis in that it does NOT show signs of [blank_start]lower[blank_end] motor neuron degeneration

Which condition has a better prognosis?

There is a strong link between ALS and which type of dementia?

Babinski Sign suggests that a patient has experienced [blank_start]upper[blank_end] motor neuron degeneration

What are the two most common causes of death in ALS patients?

The pathological hallmark of ALS is the presence of [blank_start]inclusion[blank_end] bodies (abnormal aggregations of protein) in the cytoplasm of motor neurons

How are reflexes affected by ALS?

[blank_start]Kennedy's[blank_end] Disease is an X-linked recessive condition of the motor neurons in the brainstem and spinal cord. Degeneration of these structures leads to weakness and muscle cramps. It is commonly misdiagnosed as ALS.

Kennedy's Disease [blank_start]only affects males[blank_end]

What is the main treatment for the respiratory failure seen in ALS patients?

Which sodium channel antagonist can be given to patients with ALS, prolonging their life by 2-3 months? [blank_start]Riluzole[blank_end]